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https://hdl.handle.net/2440/58280
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dc.contributor.author | Rahman, A. | - |
dc.contributor.author | Madge, S. | - |
dc.contributor.author | Billing, K. | - |
dc.contributor.author | Anderson, P. | - |
dc.contributor.author | Leibovitch, I. | - |
dc.contributor.author | Selva-Nayagam, D. | - |
dc.contributor.author | David, D. | - |
dc.date.issued | 2009 | - |
dc.identifier.citation | Eye, 2009; 23(12):2175-2181 | - |
dc.identifier.issn | 0950-222X | - |
dc.identifier.issn | 1476-5454 | - |
dc.identifier.uri | http://hdl.handle.net/2440/58280 | - |
dc.description.abstract | Aim: To present the clinical features and management outcomes in a large longitudinal series of patients with craniofacial fibrous dysplasia (CFD). Methods: Retrospective interventional consecutive case series. Main outcome measures included signs and symptoms, radiographic findings, long-term outcomes, and postoperative complications. Results: A total of 42 patients with CFD were identified. The mean age at presentation was 16.7 years; mean follow-up was 12.6 years. Out of these 42 patients, 37 (88.1%) had unilateral involvement and 5 (11.9%) had bilateral involvement, of which 3 (7.1%) had McCune–Albright syndrome. The commonest presenting symptom was facial asymmetry (36 cases, 86%). The frontal bone was the most commonly involved (27 cases, 64.3%), zfollowed by the sphenoid (24 cases, 57.1%). The most common pattern of bone involvement was monostotic (32 cases, 76.2%). Radiological optic canal involvement occurred in 18 eyes of 15 (37.5%) patients, with optic atrophy in 9 eyes (18.8%) of 7 patients (16.7%). Surgical intervention was performed in 30 (71.4%) cases for both functional and reconstructive reasons. Optic canal decompression was performed in three cases, in all of which stabilization of vision was achieved; no patient lost vision as a result of surgery. Conclusions: In this large longitudinal series of CFD, visual loss was not uncommon and occurred insidiously. The presenting clinical and radiological features, surgical interventions, and outcomes are discussed. | - |
dc.description.statementofresponsibility | AMA Rahman, SN Madge, K Billing, PJ Anderson, I Leibovitch, D Selva and D David | - |
dc.description.uri | http://www.nature.com/eye/journal/v23/n12/abs/eye20096a.html | - |
dc.language.iso | en | - |
dc.publisher | Nature Publishing Group | - |
dc.rights | © 2009 Macmillan Publishers Limited. All rights reserved | - |
dc.source.uri | http://dx.doi.org/10.1038/eye.2009.6 | - |
dc.subject | fibrous dysplasia | - |
dc.subject | optic neuropathy | - |
dc.subject | optic canal decompression | - |
dc.title | Craniofacial fibrous dysplasia: clinical characteristics and long-term outcomes | - |
dc.type | Journal article | - |
dc.identifier.doi | 10.1038/eye.2009.6 | - |
pubs.publication-status | Published | - |
dc.identifier.orcid | Anderson, P. [0000-0002-3730-4652] | - |
dc.identifier.orcid | Selva-Nayagam, D. [0000-0002-2169-5417] | - |
Appears in Collections: | Aurora harvest 5 Opthalmology & Visual Sciences publications |
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