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https://hdl.handle.net/2440/90284
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dc.contributor.author | Chummun, S. | - |
dc.contributor.author | McLean, N. | - |
dc.contributor.author | Nugent, M. | - |
dc.contributor.author | Anderson, P. | - |
dc.contributor.author | David, D. | - |
dc.date.issued | 2012 | - |
dc.identifier.citation | Journal of Craniofacial Surgery, 2012; 23(4):986-990 | - |
dc.identifier.issn | 1049-2275 | - |
dc.identifier.issn | 1536-3732 | - |
dc.identifier.uri | http://hdl.handle.net/2440/90284 | - |
dc.description.abstract | Patients with chondrodysplasia punctata (CDP) usually present with Binder-type features, and often CDP is misdiagnosed as Binder syndrome. This study reviewed the management and outcome of patients with Binder syndrome and CDP in a multidisciplinary setting. METHODS: The notes and radiographs of the patients managed at the Australian Craniofacial Unit with a multidisciplinary setting since 1976 were reviewed, and data were collected on patient demographics, associated medical and surgical problems, subsequent management, and complications. RESULTS: Seventy-seven patients were treated over the 30-year period (5 patients were lost to follow-up); of the remaining 72 patients, 60 (83%) had Binder syndrome, and 12 (17%) were patients with CDP. Forty were males, and 32 were females, with an age range of 6 months to 47 years. Thirteen patients (18%) had a strong family history, and 65 patients (90%) have so far undergone surgical correction, and of those, 35 (54%) have completed their treatment, the longest follow-up time being 18 years. The mean number of surgical procedures was 2.4, and 18 patients (28%) had postoperative complications, which included partial necrosis of the maxilla, osteomyelitis of the mandible, facial nerve and inferior alveolar nerve neuropraxia, nasal bone graft exposure, and cellulitis. DISCUSSION: Because of the phenotypic characteristics shared by both Binder syndrome and CDP, it is most likely that Binder syndrome is not a syndrome, nor is it an entity, but most likely to be an "association." We would advocate that these patients should be managed in a multidisciplinary setting. | - |
dc.description.statementofresponsibility | Shaheel Chummun, N.R. McLean, M. Nugent, P. J. Anderson and David J. David | - |
dc.language.iso | en | - |
dc.publisher | Lippincott, Williams & Wilkins | - |
dc.rights | © 2012 Mutaz B. Habal, MD | - |
dc.source.uri | http://dx.doi.org/10.1097/scs.0b013e31824e2683 | - |
dc.subject | Binder syndrome | - |
dc.subject | chondrodysplasia punctata | - |
dc.subject | costochondral nasal grafts | - |
dc.title | Binder syndrome | - |
dc.type | Journal article | - |
dc.identifier.doi | 10.1097/SCS.0b013e31824e2683 | - |
pubs.publication-status | Published | - |
dc.identifier.orcid | Anderson, P. [0000-0002-3730-4652] | - |
Appears in Collections: | Aurora harvest 7 Paediatrics publications |
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